Fabry's disease: alpha-galactosidase deficiency

JA Kint - Science, 1970 - science.org
JA Kint
Science, 1970science.org
The leukocytes of male patients with Fabry's disease are deficient in α-galactosidase. The α-
galactosidase activity in the leukocytes of female carriers of the disease is 15 to 40 percent
of the amount present in normal leukocytes. The activities of β-galactosidase, β-
acetylgalactosaminidase, and β-acetylglucosaminidase in the leukocytes of affected
individuals are normal.
The leukocytes of male patients with Fabry's disease are deficient in α-galactosidase. The α-galactosidase activity in the leukocytes of female carriers of the disease is 15 to 40 percent of the amount present in normal leukocytes. The activities of β-galactosidase, β-acetylgalactosaminidase, and β-acetylglucosaminidase in the leukocytes of affected individuals are normal.
AAAS