The prevalence of primary dystonia in the general community

J Muller, S Kiechl, GK Wenning, K Seppi, J Willeit… - Neurology, 2002 - AAN Enterprises
J Muller, S Kiechl, GK Wenning, K Seppi, J Willeit, A Gasperi, J Wissel, T Gasser, W Poewe
Neurology, 2002AAN Enterprises
The prevalence of primary dystonia was assessed in a random population sample of
individuals aged 50 and over in Bruneck, South Tyrol. The diagnosis of primary dystonia
was confirmed by videotaped review. Primary dystonia was present in 6 of 707 cases
resulting in a prevalence rate of 732 per 100,000 (95% CI 319–1,564) in the general
population aged 50 and over. Only two cases (33%) had been previously diagnosed. These
results indicate that the true prevalence of primary dystonia is significantly higher than …
The prevalence of primary dystonia was assessed in a random population sample of individuals aged 50 and over in Bruneck, South Tyrol. The diagnosis of primary dystonia was confirmed by videotaped review. Primary dystonia was present in 6 of 707 cases resulting in a prevalence rate of 732 per 100,000 (95% CI 319–1,564) in the general population aged 50 and over. Only two cases (33%) had been previously diagnosed. These results indicate that the true prevalence of primary dystonia is significantly higher than published rates.
American Academy of Neurology