Objectives To describe the features, natural history, and management of an unusual
manifestation of ocular von Hippel-Lindau disease in the form of fine vascular proliferation.
Methods Case series of 14 patients with definite or presumed von Hippel-Lindau disease.
Results Retinal vascular proliferation consisting of fine superficial vessels was found in 16
eyes of 14 patients with von Hippel-Lindau disease. The lesion was often found in a
juxtapapillary location and associated with a fibrovascular component and/or a macular …