Crystal structure of HLA-DQ0602 that protects against type 1 diabetes and confers strong susceptibility to narcolepsy

C Siebold, BE Hansen, JR Wyer… - Proceedings of the …, 2004 - National Acad Sciences
C Siebold, BE Hansen, JR Wyer, K Harlos, RE Esnouf, A Svejgaard, JI Bell, JL Strominger
Proceedings of the National Academy of Sciences, 2004National Acad Sciences
The MHC class II molecule DQ0602 confers strong susceptibility to narcolepsy but dominant
protection against type 1 diabetes. The crystal structure of DQ0602 reveals the molecular
features underlying these contrasting genetic properties. Structural comparisons to
homologous DQ molecules with differential disease associations highlight a previously
unrecognized interplay between the volume of the P6 pocket and the specificity of the P9
pocket, which implies that presentation of an expanded peptide repertoire is critical for …
The MHC class II molecule DQ0602 confers strong susceptibility to narcolepsy but dominant protection against type 1 diabetes. The crystal structure of DQ0602 reveals the molecular features underlying these contrasting genetic properties. Structural comparisons to homologous DQ molecules with differential disease associations highlight a previously unrecognized interplay between the volume of the P6 pocket and the specificity of the P9 pocket, which implies that presentation of an expanded peptide repertoire is critical for dominant protection against type 1 diabetes. In narcolepsy, the volume of the P4 pocket appears central to the susceptibility, suggesting that the presentation of a specific peptide population plays a major role.
National Acad Sciences