Myocardial involvement in the Marfan syndrome
Y FUJISEKI, K OKUNO, M TANAKA… - Japanese heart …, 1985 - jstage.jst.go.jp
Y FUJISEKI, K OKUNO, M TANAKA, M SHIMADA, M TAKAHASHI, K KAWANISHI
Japanese heart journal, 1985•jstage.jst.go.jpSUMMARY A patient with the Marfan syndrome and echocardiographic and
angiocardiographic evidence of hypertrophic cardiomyopathy is presented. Endomyocardial
biopsy was performed. Histologic abnormalities of the endomyocardium noted in this patient
were considered to be related to the basic generalized connective tissue abnormality, and
the patient subsequently developed myocardial disease compatible with hypertrophic non-
obstructive cardiomyopathy. We believe that this case emphasizes the possible coexistance …
angiocardiographic evidence of hypertrophic cardiomyopathy is presented. Endomyocardial
biopsy was performed. Histologic abnormalities of the endomyocardium noted in this patient
were considered to be related to the basic generalized connective tissue abnormality, and
the patient subsequently developed myocardial disease compatible with hypertrophic non-
obstructive cardiomyopathy. We believe that this case emphasizes the possible coexistance …
Summary
A patient with the Marfan syndrome and echocardiographic and angiocardiographic evidence of hypertrophic cardiomyopathy is presented. Endomyocardial biopsy was performed. Histologic abnormalities of the endomyocardium noted in this patient were considered to be related to the basic generalized connective tissue abnormality, and the patient subsequently developed myocardial disease compatible with hypertrophic non-obstructive cardiomyopathy. We believe that this case emphasizes the possible coexistance of subclinical myocardial disease in patients with the Marfan syndrome.
jstage.jst.go.jp