IN 1951 Binkley and Johnson¹ reported the case of a thirty-one-year-old woman with basal-cell nevi, agenesis of the corpus callosum and dental cysts. The skin lesions, appearing in childhood, extended to involve the neck, face, thorax, abdomen, upper arms and back. The jaw lesions, noted when she was about sixteen years of age, were diagnosed as dentigerous cysts. She was given roentgenotherapy to the jaw for seven years. Subsequently, fibrosarcoma developed in this area and metastasized to the lungs and vertebras, resulting in death. A fibroma of the ovary was surgically removed, and bifid sixth rib and absence of the . . .