Neutropenia associated with primary immunodeficiency syndromes
B Cham, MA Bonilla, J Winkelstein - Seminars in hematology, 2002 - Elsevier
The primary immunodeficiency diseases are a heterogeneous group of more than 75
disorders characterized by intrinsic defects in the functions of the immune system. Many are
associated with abnormalities of hematopoiesis as well. This article will review those primary
immunodeficiency syndromes in which neutropenia is a prominent finding, including X-
linked agammaglobulinemia (XLA), hyper IgM syndrome, common variable
immunodeficiency (CVID), IgA deficiency, cartilage-hair hypoplasia (CHH), and reticular …
disorders characterized by intrinsic defects in the functions of the immune system. Many are
associated with abnormalities of hematopoiesis as well. This article will review those primary
immunodeficiency syndromes in which neutropenia is a prominent finding, including X-
linked agammaglobulinemia (XLA), hyper IgM syndrome, common variable
immunodeficiency (CVID), IgA deficiency, cartilage-hair hypoplasia (CHH), and reticular …