Long QT syndrome
AJ Moss - Jama, 2003 - jamanetwork.com
THE LONG QT SYNDROME (LQTS) was first described in 1957 in a family in which several
children with congenital bilateral neural deafness and QT prolongation on
electrocardiogram (ECG) experienced recurrent syncope and sudden death, with a family
pattern that suggested autosomal recessive inheritance (Jervell and Lange-Nielsen
syndrome). 1 A similar and much more common familial disorder with QT prolongation but
without deafness was described a few years later, with family patterns that suggested …
children with congenital bilateral neural deafness and QT prolongation on
electrocardiogram (ECG) experienced recurrent syncope and sudden death, with a family
pattern that suggested autosomal recessive inheritance (Jervell and Lange-Nielsen
syndrome). 1 A similar and much more common familial disorder with QT prolongation but
without deafness was described a few years later, with family patterns that suggested …