The essential phenotypic features of the nevoid basal-cell carcinoma syndrome" have been
recognized during the hundred years since the first cases were described by Jarisch (99)
and White (210). Patients show characteristic facies, which together with enlarged calvaria
may lead the clinician to search for the nevoid basal-cell carcinoma syndrome very early in
life, even in the absence of an indicative family history. Although the syndrome has been
well defined for over 25 years, many clinicians are familiar only with its major manifestations …