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In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.
R C Rubenstein, … , M E Egan, P L Zeitlin
R C Rubenstein, … , M E Egan, P L Zeitlin
Published November 15, 1997
Citation Information: J Clin Invest. 1997;100(10):2457-2465. https://doi.org/10.1172/JCI119788.
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Research Article

In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.

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Abstract

Research Article

Authors

R C Rubenstein, M E Egan, P L Zeitlin

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