Cardiac abnormalities in myotonic dystrophy: electrophysiologic and histopathologic studies

J Motta, C Guilleminault, M Billingham, W Barry… - The American Journal of …, 1979 - Elsevier
Eight young adult male patients with myotonic dystrophy, mean age 26 years, underwent 24-
hour Holter electrocardiographic monitoring and intracardiac electrophysiologic study. Right
ventricular endomyocardial biopsies were performed at the end of the electrophysiologic
study in five of them. The atrial to His (AH) interval was 155 msec in one case and≤ 130
msec in the remaining seven. The His to ventricle interval (HV) was≥ 55 msec in all
patients. Twenty-four hour Holter electrocardiographic monitoring demonstrated more than 4 …