Characterization of connective tissue disease-associated pulmonary arterial hypertension from REVEAL: identifying systemic sclerosis as a unique phenotype

L Chung, J Liu, L Parsons, PM Hassoun, M McGoon… - Chest, 2010 - Elsevier
Background REVEAL (the Registry to Evaluate Early and Long-term Pulmonary Arterial
Hypertension Disease Management) is the largest US cohort of patients with pulmonary
arterial hypertension (PAH) confirmed by right-sided heart catheterization (RHC), providing
a more comprehensive subgroup characterization than previously possible. We used
REVEAL to analyze the clinical features of patients with connective tissue disease-
associated PAH (CTD-APAH). Methods All newly and previously diagnosed patients with …