ENU mutagenesis identifies mice with mitochondrial branched-chain aminotransferase deficiency resembling human maple syrup urine disease
J. Clin. Invest. Jer-Yuarn Wu, et al. 113:434 doi:10.1172/JCI19574 [Go to this article.]

Figure 3
Western blot analysis of BCAT-2 in control (C) and affected (A) mouse tissues. Each lane contains 10 0g of total protein from tissue extracts. Recombinant human BCAT-2 (recBCAT-2; 0.7 μg) was used as a standard.