ENU mutagenesis identifies mice with mitochondrial branched-chain aminotransferase deficiency resembling human maple syrup urine disease
J. Clin. Invest. Jer-Yuarn Wu, et al. 113:434 doi:10.1172/JCI19574 [Go to this article.]

Figure 1
Schematic catabolic pathway of branched-chain amino acids valine (Val), leucine (Leu), and isoleucine (Ile). MCF, mitochondrial carrier family.